1/12/2024 0 Comments Pierre robin sequence adultsHowever, no posterior rib gap defects were observed on PA chest radiography. The patient in this report was suspected of having CCMS because she had PRS and severe scoliosis. 7 Because the most consistent features of CCMS are associated with the hard tissues of the maxillofacial and thoracic vertebral area, radiographic evaluation, such as thoracic computed tomography, posteroanterior (PA) chest radiography, lateral cephalograms, and cone-beam computed tomography (CBCT), is required for the diagnosis and treatment planning of CCMS. The heart, the kidneys, hearing ability, and intelligence are also affected in some patients with CCMS. 5 In addition to PRS and multiple rib gaps, scoliosis is a common feature of CCMS. 4 in 1966, over 80 cases have been reported to date. 4, 5, 6 Since the first report of CCMS by Smith et al. 3 found that 60% of cases of PRS were associated with another syndrome, while 40% were isolated.Ĭerebro-costo-mandibular syndrome (CCMS) is a PRS-related syndrome associated with rib anomalies characterized by posterior rib gap defects. PRS does not always have a single pathogenesis, but rather is often associated with various syndromes. 1 This disorder, now known as Pierre Robin sequence (PRS), has received much attention in dentistry due to its relationship with anomalies in the maxillofacial area. In 1923, the dentist Pierre Robin described a disorder characterized as a triad of micrognathia, glossoptosis, and airway obstruction.
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